Q00 Anencephaly and similar malformations

Not billable (header)Chapter 17

Report one of the more specific codes below.

Check coverage with this diagnosis

Codes under this one

Q00.0 Anencephaly
Q00.1 Craniorachischisis
Q00.2 Iniencephaly

Instructional notes

Chapter 17

Excludes2Not included here: the patient may have both; report both when both are present.

inborn errors of metabolism (E70-E88)

Notes

Codes from this chapter are not for use on maternal records

Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1) · Q00-Q07 Congenital malformations of the nervous system (Q00-Q07)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.