Q85.0 Neurofibromatosis (nonmalignant)

Not billable (header)Chapter 17

Report one of the more specific codes below.

Check coverage with this diagnosis

Codes under this one

Q85.00 Neurofibromatosis, unspecified
Q85.01 Neurofibromatosis, type 1
Q85.02 Neurofibromatosis, type 2
Q85.03 Schwannomatosis
Q85.09 Other neurofibromatosis

Instructional notes

Chapter 17

Excludes2Not included here: the patient may have both; report both when both are present.

inborn errors of metabolism (E70-E88)

Notes

Codes from this chapter are not for use on maternal records

Q85

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.

ataxia telangiectasia [Louis-Bar] (G11.3)
familial dysautonomia [Riley-Day] (G90.1)

Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1) · Q80-Q89 Other congenital malformations (Q80-Q89)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.