E00 Congenital iodine-deficiency syndrome

Not billable (header)Chapter 4

Report one of the more specific codes below.

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Codes under this one

E00.0 Congenital iodine-deficiency syndrome, neurological type
E00.1 Congenital iodine-deficiency syndrome, myxedematous type
E00.2 Congenital iodine-deficiency syndrome, mixed type
E00.9 Congenital iodine-deficiency syndrome, unspecified

Instructional notes

Chapter 4

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.

transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Notes

All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

This code

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.

subclinical iodine-deficiency hypothyroidism (E02)

Use additional codeAdd a second code for the full picture.

code (F70-F79) to identify associated intellectual disabilities.

Chapter 4: Endocrine, nutritional and metabolic diseases · E00-E07 Disorders of thyroid gland (E00-E07)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.