Q01 Encephalocele

Not billable (header)Chapter 17

Report one of the more specific codes below.

Check coverage with this diagnosis

Codes under this one

Q01.0 Frontal encephalocele
Q01.1 Nasofrontal encephalocele
Q01.2 Occipital encephalocele
Q01.8 Encephalocele of other sites
Q01.9 Encephalocele, unspecified

Instructional notes

Chapter 17

Excludes2Not included here: the patient may have both; report both when both are present.

inborn errors of metabolism (E70-E88)

Notes

Codes from this chapter are not for use on maternal records

This code

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.

Meckel-Gruber syndrome (Q61.9)

Includes

Arnold-Chiari syndrome, type III
encephalocystocele
encephalomyelocele
hydroencephalocele
hydromeningocele, cranial
meningocele, cerebral
meningoencephalocele

Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1) · Q00-Q07 Congenital malformations of the nervous system (Q00-Q07)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.