Coding and coverage · ICD-10-CM

Q03 Congenital hydrocephalus

Not billable (header)Chapter 17

Report one of the more specific codes below.

Check coverage with this diagnosis

Codes under this one

  • Q03.0 Malformations of aqueduct of Sylvius
  • Q03.1 Atresia of foramina of Magendie and Luschka
  • Q03.8 Other congenital hydrocephalus
  • Q03.9 Congenital hydrocephalus, unspecified

Instructional notes

Chapter 17

Excludes2Not included here: the patient may have both; report both when both are present.
  • inborn errors of metabolism (E70-E88)
Notes
  • Codes from this chapter are not for use on maternal records

This code

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.
  • Arnold-Chiari syndrome, type II (Q07.0-)
  • acquired hydrocephalus (G91.-)
  • hydrocephalus due to congenital toxoplasmosis (P37.1)
  • hydrocephalus with spina bifida (Q05.0-Q05.4)
Includes
  • hydrocephalus in newborn

Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1) · Q00-Q07 Congenital malformations of the nervous system (Q00-Q07)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.