Coding and coverage · ICD-10-CM

Q42 Congenital absence, atresia and stenosis of large intestine

Not billable (header)Chapter 17

Report one of the more specific codes below.

Codes under this one

  • Q42.0 Congenital absence, atresia and stenosis of rectum with fistula
  • Q42.1 Congenital absence, atresia and stenosis of rectum without fistula
  • Q42.2 Congenital absence, atresia and stenosis of anus with fistula
  • Q42.3 Congenital absence, atresia and stenosis of anus without fistula
  • Q42.8 Congenital absence, atresia and stenosis of other parts of large intestine
  • Q42.9 Congenital absence, atresia and stenosis of large intestine, part unspecified

Instructional notes

Chapter 17

Excludes2Not included here: the patient may have both; report both when both are present.
  • inborn errors of metabolism (E70-E88)
Notes
  • Codes from this chapter are not for use on maternal records

This code

Includes
  • congenital obstruction, occlusion and stricture of large intestine

Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1) · Q38-Q45 Other congenital malformations of the digestive system (Q38-Q45)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.