Coding and coverage · ICD-10-CM

Q56 Indeterminate sex and pseudohermaphroditism

Not billable (header)Chapter 17

Report one of the more specific codes below.

Codes under this one

  • Q56.0 Hermaphroditism, not elsewhere classified
  • Q56.1 Male pseudohermaphroditism, not elsewhere classified
  • Q56.2 Female pseudohermaphroditism, not elsewhere classified
  • Q56.3 Pseudohermaphroditism, unspecified
  • Q56.4 Indeterminate sex, unspecified

Instructional notes

Chapter 17

Excludes2Not included here: the patient may have both; report both when both are present.
  • inborn errors of metabolism (E70-E88)
Notes
  • Codes from this chapter are not for use on maternal records

Section Q50-Q56

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.
  • androgen insensitivity syndrome (E34.5-)
  • syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)

This code

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.
  • 46,XX true hermaphrodite (Q99.1)
  • androgen insensitivity syndrome (E34.5-)
  • chimera 46,XX/46,XY true hermaphrodite (Q99.0)
  • female pseudohermaphroditism with adrenocortical disorder (E25.-)
  • pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
  • pure gonadal dysgenesis (Q99.1)

Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1) · Q50-Q56 Congenital malformations of genital organs (Q50-Q56)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.