Coding and coverage · ICD-10-CM

Q85

Q85.8 Other phakomatoses, not elsewhere classified

Not billable (header)Chapter 17

Report one of the more specific codes below.

Check coverage with this diagnosis

Codes under this one

  • Q85.81 PTEN hamartoma tumor syndrome
  • Q85.82 Other Cowden syndrome
  • Q85.83 Von Hippel-Lindau syndrome
  • Q85.89 Other phakomatoses, not elsewhere classified

Instructional notes

Chapter 17

Excludes2Not included here: the patient may have both; report both when both are present.
  • inborn errors of metabolism (E70-E88)
Notes
  • Codes from this chapter are not for use on maternal records

Q85

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.
  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • familial dysautonomia [Riley-Day] (G90.1)

This code

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.
  • Meckel-Gruber syndrome (Q61.9)

Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1) · Q80-Q89 Other congenital malformations (Q80-Q89)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.