Coding and coverage · ICD-10-CM

Q87 Other specified congenital malformation syndromes affecting multiple systems

Not billable (header)Chapter 17

Report one of the more specific codes below.

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Codes under this one

  • Q87.0 Congenital malformation syndromes predominantly affecting facial appearance
  • Q87.1 Congenital malformation syndromes predominantly associated with short statureHeader
  • Q87.2 Congenital malformation syndromes predominantly involving limbs
  • Q87.3 Congenital malformation syndromes involving early overgrowth
  • Q87.4 Marfan syndromeHeader
  • Q87.5 Other congenital malformation syndromes with other skeletal changes
  • Q87.8 Other specified congenital malformation syndromes, not elsewhere classifiedHeader
  • Q87.A Loeys-Dietz syndrome

Instructional notes

Chapter 17

Excludes2Not included here: the patient may have both; report both when both are present.
  • inborn errors of metabolism (E70-E88)
Notes
  • Codes from this chapter are not for use on maternal records

This code

Use additional codeAdd a second code for the full picture.
  • code(s) to identify all associated manifestations

Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1) · Q80-Q89 Other congenital malformations (Q80-Q89)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.