Coding and coverage · ICD-10-CM

Q87

Q87.8 Other specified congenital malformation syndromes, not elsewhere classified

Not billable (header)Chapter 17

Report one of the more specific codes below.

Codes under this one

  • Q87.81 Alport syndrome
  • Q87.82 Arterial tortuosity syndrome
  • Q87.83 Bardet-Biedl syndrome
  • Q87.84 Laurence-Moon syndrome
  • Q87.85 MED13L syndrome
  • Q87.86 Kleefstra syndrome
  • Q87.87 Hao-Fountain Syndrome
  • Q87.88 CTNNB1 syndrome
  • Q87.89 Other specified congenital malformation syndromes, not elsewhere classified

Instructional notes

Chapter 17

Excludes2Not included here: the patient may have both; report both when both are present.
  • inborn errors of metabolism (E70-E88)
Notes
  • Codes from this chapter are not for use on maternal records

Q87

Use additional codeAdd a second code for the full picture.
  • code(s) to identify all associated manifestations

This code

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.

Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1) · Q80-Q89 Other congenital malformations (Q80-Q89)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.