Coding and coverage · ICD-10-CM

G71

G71.3 Mitochondrial myopathy, not elsewhere classified

BillableNo payment HCCChapter 6

Instructional notes

Chapter 6

Excludes2Not included here: the patient may have both; report both when both are present.
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

G71

Excludes2Not included here: the patient may have both; report both when both are present.
  • arthrogryposis multiplex congenita (Q74.3)
  • metabolic disorders (E70-E88)
  • myositis (M60.-)

This code

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.
  • Kearns-Sayre syndrome (H49.81)
  • Leber's disease (H47.21)
  • Leigh's encephalopathy (G31.82)
  • mitochondrial metabolism disorders (E88.4.-)
  • Reye's syndrome (G93.7)

Chapter 6: Diseases of the nervous system · G70-G73 Diseases of myoneural junction and muscle (G70-G73)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.