Coding and coverage · ICD-10-CM

I27 › I27.2

I27.21 Secondary pulmonary arterial hypertension

BillableCMS-HCC V28: HCC 226Chapter 9
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Instructional notes

Chapter 9

Excludes2Not included here: the patient may have both; report both when both are present.
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • transient cerebral ischemic attacks and related syndromes (G45.-)

I27.2

Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.
  • Eisenmenger's syndrome (I27.83)
Code also
  • associated underlying condition

This code

Code also
  • associated conditions if applicable, or adverse effects of drugs or toxins, such as:
  • adverse effect of appetite depressants (T50.5X5)
  • congenital heart disease (Q20-Q28)
  • human immunodeficiency virus [HIV] disease (B20)
  • polymyositis (M33.2-)
  • portal hypertension (K76.6)
  • rheumatoid arthritis (M05.-)
  • schistosomiasis (B65.-)
  • Sjögren syndrome (M35.0-)
  • systemic sclerosis (M34.-)
Inclusion terms
  • (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
  • (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension

Chapter 9: Diseases of the circulatory system · I26-I28 Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)

Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.

Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.