Coding and coverage · ICD-10-CM
Instructional notes
Chapter 9
Excludes2Not included here: the patient may have both; report both when both are present.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- systemic connective tissue disorders (M30-M36)
- transient cerebral ischemic attacks and related syndromes (G45.-)
I27.2
Excludes1Not coded here: never report with this code, except when the two conditions are unrelated.
- Eisenmenger's syndrome (I27.83)
Code also
- associated underlying condition
This code
Code also
- other associated disorders, if known, such as:
- chronic myeloid leukemia (C92.10-C92.22)
- essential thrombocythemia (D47.3)
- Gaucher disease (E75.22)
- hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
- hyperthyroidism (E05.-)
- hypothyroidism (E00-E03)
- polycythemia vera (D45)
- sarcoidosis (D86.-)
Inclusion terms
- Group 5 pulmonary hypertension
- Pulmonary hypertension with unclear multifactorial mechanisms
- Pulmonary hypertension due to hematologic disorders
- Pulmonary hypertension due to metabolic disorders
- Pulmonary hypertension due to other systemic disorders
Chapter 9: Diseases of the circulatory system · I26-I28 Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)
Source: ICD-10-CM FY 2027 code descriptions and tabular list (CMS and CDC National Center for Health Statistics), effective 2026-10-01 through 2027-09-30 · CMS ICD-10 files. HCC mapping: CMS-HCC V28, payment year 2027. As of 2026-11-04.
Coverage and payment depend on the claim details; confirm with the Medicare Administrative Contractor.